EOS (Idiopathic) 

Background 

  • Infantile <4 
  • Juvenile 4-10 
  • Natural history: 
    • Infantile spontaneous resolution in many (esepcially infantile) 
    • Juvenile high requirement of surgery 
  • M>F 
  • Left thoracic 

Risk of Progression 

  • Radiographic 
    • Rib – Vert overlap at apical – high risk 
    • RVAD – rib – vert angle difference – >20 high risk 

Investigation 

  • Higher incidence of neural axis anomaly 
    • Syringomyelia (cyst in cord) 
    • Chiai (cerebella tonsil protrude through bases of skull opening – CSF outflow blocked) 
    • Tethered cord 
    • Dysraphism 
  • MRI in children <10 with curve >20 

Risk of neural axis abnormality in Juvenile idiopathic scoliosis? 

less than 10% 

15% to 30% 

45% to 60% 

greater than 60% 

Management 

  • Observation 
    • Most resolve spontaneously 
  • RVAD >20 or Rib Vert overlap -> Serial Mehta casting 
    • Milwaukee brace after to maintain 
  • Operative 
    • Indications: 
      • Cobb >50 
      • Failed Mehta 
    • Timing: 
      • Before age 8 to maximize FVC 
      • Fusion close to skeletal maturity 

Operative Options 

  • Growing Rod 
    • Growing Rods 
    • Lengthen q 6 months 
  • VEPTR – for TIS 
    • Rib to rib 
    • Rib to pelvis 
  • Eventual definitive fusion at skeletal maturity  

Pulmonary Function 

  • Alveolar multiplication happen up to age 8 
  • 18cm minimum thoracic height, 22 is goal 
  • FVC correlated to % of spine fused 
  • PFT <45% inc mortality 
  • RF worse FVC 
    • Fusion to T1-2 
    • PT kyphosis >4 segments 
    • Rib deformity 
    • Extent of fusion