Background
- Infantile <4
- Juvenile 4-10
- Natural history:
- Infantile spontaneous resolution in many (esepcially infantile)
- Juvenile high requirement of surgery
- M>F
- Left thoracic
Risk of Progression
- Radiographic
- Rib – Vert overlap at apical – high risk
- RVAD – rib – vert angle difference – >20 high risk
Investigation
- Higher incidence of neural axis anomaly
- Syringomyelia (cyst in cord)
- Chiai (cerebella tonsil protrude through bases of skull opening – CSF outflow blocked)
- Tethered cord
- Dysraphism
- MRI in children <10 with curve >20
Risk of neural axis abnormality in Juvenile idiopathic scoliosis?
less than 10%
15% to 30%
45% to 60%
greater than 60%
Management
- Observation
- Most resolve spontaneously
- RVAD >20 or Rib Vert overlap -> Serial Mehta casting
- Milwaukee brace after to maintain
- Operative
- Indications:
- Cobb >50
- Failed Mehta
- Timing:
- Before age 8 to maximize FVC
- Fusion close to skeletal maturity
- Indications:
Operative Options
- Growing Rod
- Growing Rods
- Lengthen q 6 months
- VEPTR – for TIS
- Rib to rib
- Rib to pelvis
- Eventual definitive fusion at skeletal maturity
Pulmonary Function
- Alveolar multiplication happen up to age 8
- 18cm minimum thoracic height, 22 is goal
- FVC correlated to % of spine fused
- PFT <45% inc mortality
- RF worse FVC
- Fusion to T1-2
- PT kyphosis >4 segments
- Rib deformity
- Extent of fusion